1.
Indian Pediatr
;
2009 Aug; 46(8): 723-725
Article
in English
| IMSEAR
| ID: sea-144156
ABSTRACT
An 8 year old boy presented with fever of unknown origin in whom the diagnosis of liver abscess was made. He also had palmoplantar keratoderma and premature loss of teeth, consistent with the diagnosis of Papillon Lefevre syndrome.
Subject(s)
Amikacin/therapeutic use , Anti-Bacterial Agents/therapeutic use , Cefotaxime/therapeutic use , Child , Dermatologic Agents/therapeutic use , Humans , Isotretinoin/therapeutic use , Liver Abscess/complications , Male , Papillon-Lefevre Disease/complications , Papillon-Lefevre Disease/drug therapy , Periodontitis/complications , Skin Diseases/complications , Skin Diseases/drug therapy , Sulbactam/therapeutic use
2.
Indian J Dermatol Venereol Leprol
;
2008 Jan-Feb; 74(1): 71-3
Article
in English
| IMSEAR
| ID: sea-52711
3.
Article
in English
| IMSEAR
| ID: sea-94723
ABSTRACT
Papillon Lefèvre syndrome is a rare disease characterized by skin lesions caused by palmar-plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. It is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one-third of cases. Pyogenic liver abscess is an increasingly recognized complication. We report a new case of this association and review the current literature.